Copyright © 2004 Elsevier Inc. All rights reserved.
Case Report
Sporadic Creutzfeldt–Jakob disease presenting with nonconvulsive
status epilepticus
David Cohen, Ekrem KutluayCorresponding Author Contact Information
,
E-mail The Corresponding Author , Jonathan
Edwards, Amanda Peltier and Ahmad Beydoun
Department of Neurology, University of Michigan Health System,
UH1B300/0036 Ann Arbor, MI 48109, USA
Received 14 May 2004; revised 25 June 2004; accepted 25 June 2004.
Available online 14 August 2004.
Abstract
Creutzfeldt–Jakob disease (CJD) is a rare prion disease characterized by
a spongiform encephalopathy in humans. Although the characteristic triad
of myoclonus, dementia, and periodic EEG activity is easy to recognize,
unusual manifestations of the disease may be challenging and create a
diagnostic dilemma. We report a case of CJD that occurred in a
26-year-old patient who presented with a receptive (Wernicke’s) aphasia
secondary to nonconvulsive status epilepticus.
Keywords: Creutzfeldt–Jakob disease; Status epilepticus; Wernicke’s aphasia
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