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From: TSS ()
Subject: 22-YEAR-OLD SUSPECT NVCJD PORTSMOUTH WOMAN DIES
Date: April 10, 2008 at 9:25 am PST

Woman who may have had rare brain disease dies in Portsmouth

By Steve Stone
The Virginian-Pilot
© April 10, 2008
PORTSMOUTH

A 22-year-old woman who may have had a rare degenerative brain disorder that
has been linked to eating beef from cattle infected with mad cow disease has
died.

A nursing supervisor said the woman, who had been unconscious at Bon Secours
Maryview Medical Center, passed away about 5:30 p.m. Wednesday.

The state health department said earlier this week that it was investigating
the case, looking to see if the woman had any of a range of neurological
disorders.

One possibility is a variant of Creutzfeldt-Jakob disease, known as vCJD, a
rare degenerative brain disorder that has been linked to consumption of
contaminated beef. The disease is not spread through casual contact from
person to person.

There are also other forms of Creutzfeldt-Jakob disease, known as CJD, that
are unrelated to beef consumption. State officials are looking into those as
well.


http://hamptonroads.com/2008/04/woman-who-may-have-had-rare-brain-disease-dies-portsmouth

vCJD
Recent news reports have linked variant Creutzfeldt-Jakob Disease to an
undetermined illness in Virginia.

Learn the facts here


http://www.vdh.state.va.us/


Frequently asked questions on variant Creutzfeldt-Jakob Disease and
Creutzfeldt-Jakob Disease
What is variant Creutzfeldt-Jakob Disease?
Variant Creutzfeldt-Jakob Disease (vCJD) is a rare and fatal human
neurodegenerative disease distinct from Creutzfeldt-Jakob Disease. Although
the two diseases similarly destroy the brain, the disorders are different.

Variant CJD is linked to the consumption of beef products from cattle with
bovine spongiform encephalopathy (BSE), a disease caused by abnormal prion
proteins and sometimes referred to as “mad cow disease.” Since the disease
was first described in 1996, at least 200 patients with this disease have
been identified. Most cases have occurred in the United Kingdom.

How does variant Creutzfeldt-Jakob Disease differ from Creutzfeldt-Jakob
Disease?
Creutzfeldt-Jakob Disease (CJD) is also a rare, fatal neurodegenerative
disease but is distinct from vCJD. This disease typically occurs among older
people, is rapidly progressive with infection leading to death usually
within a year of the onset of illness, while vCJD is less rapid and often
strikes younger adults. CJD is not related to beef consumption.

About 85 percent of CJD cases occur for unknown reasons while about 5-15
percent of patients develop CJD because of inherited genetic mutations. CJD
strikes about one in one million people, or about 200 people a year
nationwide.

Both CJD and vCJD are prion diseases, a group of rare, invariably fatal
brain disorders which occur both in humans and certain animals. Diagnosis of
either disease is very difficult and often happens through a process of
elimination of other disorders.

Are there other things that can cause similar symptoms?

Degenerative diseases of the brain are characterized by changes in brain
function and structure and can vary in severity. There is a wide variety of
causes of these symptoms including infections from bacteria or viruses; lack
of oxygen to the brain; liver or kidney failure; toxic exposures to
substances such as solvents, paints or industrial chemicals; and poor
nutrition.

Is there any treatment for vCJD or CJD?

There is no known treatment for either disease.

How are the diseases diagnosed?

Confirmation of a diagnosis of vCJD or CJD generally is by brain biopsy or
autopsy and the analysis takes weeks to complete. Tests that can help
develop a diagnosis include an electroencephalogram (EEG) to see if the
brain’s electrical pattern shows specific abnormalities. Magnetic resonance
imaging (MRI) scans also can reveal characteristic patterns of brain
degeneration. Cerebrospinal fluid can be examined for proteins related to
neurodegenerative diseases. A biopsy of the tonsils is also sometimes
helpful in establishing a diagnosis.

Have there been cases of vCJD in the United States?

As of April 9, 2008, three cases of vCJD have been reported from the United
States. According to the Centers for Disease Control and Prevention, there
is strong evidence suggesting that two of the three cases were exposed to
the BSE agent in the United Kingdom and that the third was exposed while
living in Saudi Arabia.

Is our food safe?

Since 1989, the Food and Drug Administration and the U.S. Department of
Agriculture have worked to reduce the risk of consumer exposure to any
BSE-contaminated material. Both agencies have issued rules to prevent the
use of mammalian protein in the manufacture of ruminant feed. There is no
current test available to identify BSE in beef. There is no evidence to
suggest that milk and dairy products can transmit the infection. Cooking and
irradiation have not been shown to kill the BSE agent.

http://www.vdh.state.va.us/news/alerts/vCJD02.htm


THIS case will be anything but nvCJD. how could it be? the victim never left
the USA, and the USA does not have BSE $$$ ...TSS


*Acquired in UK
** Acquired in Saudi Arabia
*** Includes 17 inconclusive and 9 pending (1 from 2006, 8 from 2007.
**** Includes 17 non-vCJD type unknown (2 from 1996, 2 from 1997, 1
from 2001, 1 from 2003, 4 from 2004, 3 from 2005, 4 from 2006) and 36
type pending (2 from 2005, 8 from 2006, 26 from 2007).

Notes:

-- Cases are listed based on the year of death when available. If the
year of death is not available, the year of sample receipt is used.

-- Referrals: Cases with possible or probable prion disease from
which brain tissue or blood in the case of familial disease were
submitted.

-- Inconclusive: Cases in which the samples were not sufficient to
make a diagnosis.

-- Non-vCJD type unknown are cases in which the tissue submitted was
adequate to establish the presence but not the type; in all cases,
vCJD could be excluded.

--

Terry S. Singeltary Sr.

[In submitting these data, Terry S. Singeltary Sr. draws attention to
the steady increase in the "type unknown" category, which, according
to their definition, comprises cases in which vCJD could be excluded.
The total of 26 cases for the current year (2007) is disturbing,
possibly symptomatic of the circulation of novel agents.
Characterization of these agents should be given a high priority. -
Mod.CP]

http://www.promedmail.org/pls/askus/f?p=2400:1001:6833194127530602005::NO::F2400_P1001_BACK_PAGE,F2400_P1001_PUB_MAIL_ID:1010,39963

There is a growing number of human CJD cases, and they were presented
last week in San Francisco by Luigi Gambatti(?) from his CJD
surveillance collection.

He estimates that it may be up to 14 or 15 persons which display
selectively SPRPSC and practically no detected RPRPSC proteins.

http://www.fda.gov/ohrms/dockets/ac/06/transcripts/1006-4240t1.htm

http://www.fda.gov/ohrms/dockets/ac/06/transcripts/2006-4240t1.pdf

JOURNAL OF NEUROLOGY

MARCH 26, 2003

RE-Monitoring the occurrence of emerging forms of Creutzfeldt-Jakob

disease in the United States

Email Terry S. Singeltary:

flounder@wt.net

I lost my mother to hvCJD (Heidenhain Variant CJD). I would like to

comment on the CDC's attempts to monitor the occurrence of emerging

forms of CJD. Asante, Collinge et al [1] have reported that BSE

transmission to the 129-methionine genotype can lead to an alternate

phenotype that is indistinguishable from type 2 PrPSc, the commonest

sporadic CJD. However, CJD and all human TSEs are not reportable

nationally. CJD and all human TSEs must be made reportable in every

state and internationally. I hope that the CDC does not continue to

expect us to still believe that the 85%+ of all CJD cases which are

sporadic are all spontaneous, without route/source. We have many TSEs in

the USA in both animal and man. CWD in deer/elk is spreading rapidly and

CWD does transmit to mink, ferret, cattle, and squirrel monkey by

intracerebral inoculation. With the known incubation periods in other

TSEs, oral transmission studies of CWD may take much longer. Every

victim/family of CJD/TSEs should be asked about route and source of this

agent. To prolong this will only spread the agent and needlessly expose

others. In light of the findings of Asante and Collinge et al, there

should be drastic measures to safeguard the medical and surgical arena

from sporadic CJDs and all human TSEs. I only ponder how many sporadic

CJDs in the USA are type 2 PrPSc?

http://www.neurology.org/cgi/eletters/60/2/176#535

THE PATHOLOGICAL PROTEIN

Hardcover, 304 pages plus photos and illustrations. ISBN 0-387-95508-9

June 2003

BY Philip Yam

CHAPTER 14 LAYING ODDS

Answering critics like Terry Singeltary, who feels that the U.S.
under-counts CJD, Schonberger conceded that the current surveillance
system has errors but stated that most of the errors will be confined
to the older population.

http://www.thepathologicalprotein.com/

doi:10.1016/S1473-3099(03)00715-1
Copyright © 2003 Published by Elsevier Ltd.
Newsdesk

Tracking spongiform encephalopathies in North America

Xavier Bosch

Available online 29 July 2003.
Volume 3, Issue 8, August 2003, Page 463

My name is Terry S Singeltary Sr, and I live in Bacliff, Texas. I lost
my mom to hvCJD (Heidenhain variant CJD) and have been searching for
answers ever since. What I have found is that we have not been told
the truth. CWD in deer and elk is a small portion of a much bigger
problem." ...

http://www.thelancet.com/journals/laninf/article/PIIS1473309903007151/fulltext

http://download.thelancet.com/pdfs/journals/1473-3099/PIIS1473309903007151.pdf

Diagnosis and Reporting of Creutzfeldt-Jakob Disease

Singeltary, Sr et al. JAMA.2001; 285: 733-734.

http://jama.ama-assn.org/http://www.neurology.org/cgi/eletters/60/2/176#535

APHIS-2006-0041-0006 TSE advisory committee for the meeting December
15, 2006

http://www.regulations.gov/fdmspublic/ContentViewer?objectId=09000064801f3413&disposition=attachment&contentType=msw8

Subject: [Docket No. FSIS-2006-0011] FSIS Harvard Risk Assessment of
Bovine Spongiform Encephalopathy (BSE)

http://www.fsis.usda.gov/OPPDE/Comments/2006-0011/2006-0011-1.pdf

[Docket No. 03-025IFA] FSIS Prohibition of the Use of Specified Risk
Materials for Human Food and Requirement for the Disposition of
Non-Ambulatory Disabled Cattle

9/13/2005

http://www.fsis.usda.gov/OPPDE/Comments/03-025IFA/03-025IFA-2.pdf

2 January 2000

British Medical Journal

U.S. Scientist should be concerned with a CJD epidemic in the U.S., as
well

http://www.bmj.com/cgi/eletters/320/7226/8/b#6117

15 November 1999

British Medical Journal

vCJD in the USA * BSE in U.S.

http://www.bmj.com/cgi/eletters/319/7220/1312/b#5406

Monitoring the occurrence of emerging forms of Creutzfeldt-Jakob
disease in the United States

http://cjdusa.blogspot.com/

Creutzfeldt Jakob Disease

http://creutzfeldt-jakob-disease.blogspot.com/

Creutzfeldt-Jakob Disease, Prion Protein Gene Codon 129VV, and a Novel
PrPSc ype in a Young British Woman

http://creutzfeldt-jakob-disease.blogspot.com/2008/01/creutzfeldt-jakob-disease-prion-protein.html

CJD QUESTIONNAIRE

http://cjdquestionnaire.blogspot.com/

ANIMAL HEALTH REPORT 2006 (BSE h-BASE EVENT IN ALABAMA, Scrapie, and CWD)

http://animalhealthreport2006.blogspot.com/

CREUTZFELDT JAKOB DISEASE MAD COW BASE UPDATE USA

http://cjdmadcowbaseoct2007.blogspot.com/

Friday, January 11, 2008

CJD HUMAN TSE REPORT UK, USA, CANADA, and Mexico JANUARY 2008

http://cjdmadcowbaseoct2007.blogspot.com/2008/01/cjd-human-tse-report-uk-usa-canada-and.html

Friday, February 8, 2008

Creutzfeldt Jakob Disease Delaware UPDATE

http://cjdmadcowbaseoct2007.blogspot.com/2008/02/creutzfeldt-jakob-disease-delaware.html

CREUTZFELDT JAKOB DISEASE TEXAS

http://cjdtexas.blogspot.com/

Friday, January 25, 2008

January 2008 Update on Feed Enforcement Activities to Limit the Spread
of BSE

http://madcowspontaneousnot.blogspot.com/2008/01/january-2008-update-on-feed-enforcement.html

http://madcowspontaneousnot.blogspot.com/

BSE BASE MAD COW TESTING TEXAS, USA, AND CANADA

http://madcowtesting.blogspot.com/

NOR-98 ATYPICAL SCRAPIE USA UPDATE AS AT OCT 2007

http://nor-98.blogspot.com/

http://scrapie-usa.blogspot.com/

Sunday, March 16, 2008

MAD COW DISEASE terminology UK c-BSE (typical), atypical BSE H or L,
and or Italian L-BASE

http://bse-atypical.blogspot.com/2008/03/mad-cow-disease-terminology-uk-c-bse.html

SCHOOL LUNCH PROGRAM FROM DOWNER CATTLE UPDATE

http://downercattle.blogspot.com/

SRM MAD COW RECALL 406 THOUSAND POUNDS CATTLE HEADS WITH TONSILS KANSAS

http://cjdmadcowbaseoct2007.blogspot.com/2008/04/srm-mad-cow-recall-406-thousand-pounds.html

SPECIFIED RISK MATERIALS

http://madcowspontaneousnot.blogspot.com/2008/02/specified-risk-materials-srm.html


DEEP THROAT TO TSS 2000-2001
(take these old snips of emails with how ever
many grains of salt you wish. ...tss)

The most frightening thing I have read all day is the
report of Gambetti's finding of a new strain of
sporadic cjd in young people...Dear God, what in
the name of all that is holy is that!!!
If the US has different strains of
scrapie.....why????than the UK...then would the same
mechanisms that make different strains of scrapie here
make different strains of BSE...if the patterns are
different in sheep and mice for scrapie.....could not
the BSE be different in the cattle, in the mink, in
the humans.......I really think the slides or tissues
and everything from these young people with the new
strain of sporadic cjd should be put up to be analyzed
by many, many experts in cjd........bse.....scrapie
Scrape the damn slide and put it into
mice.....wait.....chop up the mouse brain and and
spinal cord........put into some more mice.....dammit
amplify the thing and start the damned
research.....This is NOT rocket science...we need to
use what we know and get off our butts and move....the
whining about how long everything takes.....well it
takes a whole lot longer if you whine for a year and
then start the research!!!
Not sure where I read this but it was a recent press
release or something like that:
I thought I would fall out of my chair when I read
about how there was no worry about infectivity from a
histopath slide or tissues because they are preserved
in formic acid, or formalin or formaldehyde.....for
God's sake........ Ask any pathologist in the UK what
the brain tissues in the formalin looks like after a
year.......it is a big fat sponge...the agent
continues to eat the brain ......you can't make slides
anymore because the agent has never stopped........and
the old slides that are stained with Hemolysin and
Eosin......they get holier and holier and degenerate
and continue...what you looked at 6 months ago is not
there........Gambetti better be photographing every
damned thing he is looking at.....

Okay, you need to know. You don't need to pass it on
as nothing will come of it and there is not a damned
thing anyone can do about it. Don't even hint at it
as it will be denied and laughed at..........
USDA is gonna do as little as possible until there is
actually a human case in the USA of the
nvcjd........if you want to move this thing along and
shake the earth....then we gotta get the victims
families to make sure whoever is doing the autopsy is
credible, trustworthy, and a saint with the courage of
Joan of Arc........I am not kidding!!!!
so, unless we get a human death from EXACTLY the same
form with EXACTLY the same histopath lesions as seen
in the UK nvcjd........forget any action........it is
ALL gonna be sporadic!!!

And, if there is a case.......there is gonna be every
effort to link it to international travel,
international food, etc. etc. etc. etc. etc. They
will go so far as to find out if a sex partner had
ever traveled to the UK/europe, etc. etc. ....
It is gonna be a long, lonely, dangerous twisted
journey to the truth. They have all the cards, all
the money, and are willing to threaten and carry out
those threats....and this may be their biggest
downfall...

Thanks as always for your help.
(Recently had a very startling revelation from a rather senior person in
government here..........knocked me out of my chair........you must keep
pushing. If I was a power person....I would be demanding that there be a
least a million bovine tested as soon as possible and agressively
seeking this disease. The big players are coming out of the woodwork as
there is money to be made!!!
In short: "FIRE AT WILL"!!! for the very dumb....who's "will"! "Will
be the burden to bare if there is any coverup!"

again it was said years ago and it should
be taken seriously....BSE will NEVER be found in the
US!
As for the BSE conference call...I think you did a
great service to freedom of information and making
some people feign integrity...I find it scary to see
that most of the "experts" are employed by the federal
government or are supported on the "teat" of federal
funds. A scary picture!
I hope there is a confidential panel organized by the
new government to really investigate this thing.

You need to watch your back........but keep picking at
them.......like a buzzard to the bone...you just may
get to the truth!!! (You probably have more support than
you know. Too many people are afraid to show you or let
anyone else know. I have heard a few things myself...
you ask the questions that everyone else is too afraid to ask.)


==========================================


http://lists.ifas.ufl.edu/cgi-bin/wa.exe?A2=ind0612&L=sanet-mg&T=0&P=10326

http://brain.hastypastry.net/forums/archive/index.php/t-5581.html


see full text ;


http://disc.server.com/discussion.cgi?disc=7498;article=3473;title=CJD%20Voice%20Discussion%20Group

https://www.blogger.com/comment.g?blogID=7842737484277562285&postID=5759550357128128100

TSS




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