Follow Ups | Post Followup | Back to Discussion Board | VegSource
See spam or
inappropriate posts?
Please let us know.

From: TSS ()
Subject: Idaho probes outbreak of Creutzfeldt-Jakob disease
Date: August 12, 2005 at 1:24 pm PST

Idaho probes outbreak of Creutzfeldt-Jakob disease
Fri Aug 12, 2005 2:32 PM ET

By Michael Kahn
SAN FRANCISCO (Reuters) - Idaho officials on Friday confirmed one case of naturally occurring Creutzfeldt-Jakob disease and are investigating five other suspected cases, but said none are believed to be caused by eating infected animals.

Tom Shanahan, a spokesman for the Idaho Department of Health and Welfare, said five of the cases were in one geographic area and involved people over the age of 60.

"It is the naturally occurring type of CJD," Shanahan said. "It is not variant."

CJD is a rare brain-wasting disease in humans that usually affects older people in their 60s or 70s. It is not the same as the human form of mad cow disease, which is known as variant Creutzfeldt-Jakob Disease and is linked to eating beef from infected cattle.

Naturally occurring CJD is found at a rate of about one case per 1 million population annually, according to the U.S. Centers for Disease Control.

Yet in a state with only 1.4 million people the fact that Idaho has so many suspected cases of the rare disease has sparked concern among officials.

Shanahan said researchers at Case Western Reserve confirmed that brain tissue from one woman showed CJD caused her death and that the state was waiting for results from two other tests. All the deaths occurred this year, beginning in February, he said.

"We actually are real concerned because we have never had more than three cases in a year and they are in one geographic area," Shanahan said.

The sixth suspected case involves an elderly man who has not yet died, he said. The disease cannot be confirmed until a brain sample is collected and analyzed after death.

Investigators so far have not been able to pinpoint any thing that may have caused the disease and are looking at such factors as the victims' diets.

In recent years, the United States has reported fewer than 300 cases of CJD each year, according to the Centers for Disease Control Continued ...

"It is not related as far as we know to eating any infected beef," Shanahan said.

Last year, health officials found a cluster of 13 deaths due to naturally occurring CJD in New Jersey between 1988 and 1992. All of those people either attended or worked at a race track in Cherry Hill, New Jersey, according to investigators.

The variant form of CJD is the human equivalent of bovine spongiform encephalopathy, or mad cow disease, and is contracted by people who eat beef from infected cattle.

The naturally occurring strain of CJD has no known cause.

However, both types are incurable diseases involving a malformed protein, or prion, that kills brain cells.

The United States has confirmed two cases of mad cow disease, one in a Washington state dairy animal in 2003 and the other in a Texas beef cow this year.

© Reuters 2005. All Rights Reserved.


Follow Ups:

Post a Followup

E-mail: (optional)


Optional Link URL:
Link Title:
Optional Image URL: